Ferreira Raquel Miriam, Vieira Luis, Pimenta Sofia, Pinto José, Costa Lúcia
Centro Hospitalar São João.
Acta Reumatol Port. 2019 Apr-Jun;44(2):163-164.
Sarcomatous degeneration is one of the serious and rare complications of Paget's disease of bone. Osteosarcoma is the most common secondary tumour, while other variants such as chondrosarcoma are extremely uncommon. We describe a unique case of Paget's chondrosarcoma of the pelvis in an elderly female patient, with no previous established diagnosis of osteitis deformans. We emphasize clinical and radiologic aspects that should raise suspicion of malignant transformation, revealing good correlation with the final histopathological diagnosis.
肉瘤样变性是骨佩吉特病严重且罕见的并发症之一。骨肉瘤是最常见的继发性肿瘤，而其他变体如软骨肉瘤则极为罕见。我们描述了一例老年女性患者骨盆佩吉特软骨肉瘤的独特病例，该患者既往未确诊畸形性骨炎。我们强调了应引起恶性转化怀疑的临床和放射学方面，显示出与最终组织病理学诊断有良好的相关性。
