新生儿暴发性脓毒症表现为白细胞黏附缺陷。
Leucocyte adhesion defect presenting as fulminant sepsis in a new born.
作者信息
Gupta Vishal, Pandita Aakash, Panghal Astha, Pillai Anish
机构信息
Neonatology, Neonest Hospital, New Delhi, India.
Neonatology, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India.
出版信息
BMJ Case Rep. 2019 Aug 30;12(8):e227065. doi: 10.1136/bcr-2018-227065.
Abstract
We present a term neonate with severe sepsis, presenting on day 10 of life. The neonate presented with bilateral purulent eye discharge and hepatosplenomegaly. On investigation, persistent leucocytosis was observed and thus the possibility of leucocyte adhesion defect was considered. Flow cytometry confirmed the diagnosis.
摘要
我们报告一例足月儿，出生后第10天出现严重脓毒症。该新生儿表现为双侧脓性眼部分泌物及肝脾肿大。经检查，发现持续性白细胞增多，因此考虑白细胞黏附缺陷的可能性。流式细胞术确诊了该诊断。
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