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一例罕见的特发性炎性肌病,表现为机化性肺炎伴空洞性病变。

An unusual case of idiopathic inflammatory myopathy presenting with organizing pneumonia as cavitary lesions.

作者信息

Agrawal Sumita, Gupta Nitesh, Kumar Rohit, Sen M K, Chakrabarti Shibdas, Suri Jagdish Chander

机构信息

Department of Pulmonary, Critical Care & Sleep Medicine, VMMC & Safdarjung Hospital, New Delhi, India.

Medeor JCS Institute of Pulmonary, Critical Care & Sleep Medicine, Qutab Institutional Area, New Delhi, India.

出版信息

Adv Respir Med. 2019;87(4):243-246. doi: 10.5603/ARM.2019.0041.

DOI:10.5603/ARM.2019.0041
PMID:31476013
Abstract

A young woman presented with gradually progressive breathlessness, cough and muscle weakness for one and a half year. Her chest radiograph showed multiple, bilateral thin-walled cavitary lesions. Her serum was found to be positive for anti-Jo1 antibodies on serology. Histopathology of lung lesions was suggestive of organizing pneumonia. The muscle biopsy demonstrated a myopathic pattern. On the basis of these findings she was diagnosed to be the case of idiopathic inflammatory myopathy. Her condition improved significantly after treatment with steroids.

摘要

一名年轻女性出现逐渐加重的呼吸困难、咳嗽和肌肉无力症状达一年半之久。她的胸部X光片显示双侧有多个薄壁空洞性病变。血清学检查发现她的血清抗Jo1抗体呈阳性。肺部病变的组织病理学提示为机化性肺炎。肌肉活检显示为肌病模式。基于这些发现,她被诊断为特发性炎性肌病。使用类固醇治疗后,她的病情显著改善。

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Adv Respir Med. 2019;87(4):243-246. doi: 10.5603/ARM.2019.0041.
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