Armas Isabel, Vidoedo José, Afonso Luís Pedro, Moreira Augusto, Abreu de Sousa Joaquim
General Surgery / Unidade Local de Saúde do Nordeste (ULSNE), Portugal.
Vascular Surgery / Centro Hospitalar Tâmega e Sousa (CHTS), Portugal.
Rev Port Cir Cardiotorac Vasc. 2019 Apr-Jun;26(2):155-157.
Ephitelioid Hemangioendothelioma (EHE) is a rare type of tumor with vascular and sarcomatous components. There's only another case published of an internal jugular vein (IJV) EHE. A case of a 50 years-old woman with a palpable and pulsatile mass on the left cervical area is reported. Doppler ultrasound and magnetic resonance imaging showed an IVJ' 4 cm mass. Cytology was inconclusive. Surgical treatment was therefore decided and during surgery a mass inside the left IJV, with local nonsuspicious lymph nodes, was confirmed. The mass was resected including a segmental resection of the IJV and one affected tributary vessel. Lymphadenectomy of the adjacent cervical levels was performed. Histologic examination depicted an EHE without metastatic lymph nodes. Tumor was staged as pT1bN0M0 and a multidisciplinary sarcoma group proposed surveillance. Patient remained well, without evidence of disease and without complications in a twenty-four months follow-up period.
上皮样血管内皮瘤（EHE）是一种罕见的具有血管和肉瘤成分的肿瘤。仅有另一例关于颈内静脉（IJV）EHE的病例发表。本文报道了一例50岁女性，其左侧颈部可触及搏动性肿块。多普勒超声和磁共振成像显示颈内静脉有一个4厘米的肿块。细胞学检查结果不明确。因此决定进行手术治疗，术中证实左侧颈内静脉内有一个肿块，局部淋巴结无异常。切除肿块，包括颈内静脉的节段性切除和一根受累的分支血管。对相邻颈部水平进行了淋巴结清扫。组织学检查显示为EHE，无转移性淋巴结。肿瘤分期为pT1bN0M0，多学科肉瘤小组建议进行监测。在24个月的随访期内，患者情况良好，无疾病证据且无并发症。
