一名患有肖恩综合征患者的左心室心肌致密化不全。

Left ventricular non-compaction in a patient with Shone's complex.

作者信息

Toufan Mehrnoush, Pourafkari Lelll, Baghbani-Oskouel Aldln, Nader Nader D

机构信息

Department of Cardiology, Cardiovascular Research Center, Tabriz University of Medical Sciences, Tabriz, Iran.

Department of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran.

出版信息

Turk Kardiyol Dern Ars. 2019 Sep;47(6):503-506. doi: 10.5543/tkda.2018.30136.

DOI:10.5543/tkda.2018.30136

PMID:31483300

Abstract

Shone's complex is a rare congenital cardiac malformation characterized by serial obstructive lesions of the left heart at multiple levels. Presently described is an unusual case of an adult male patient who presented with palpitations and worsening dyspnea. An echocardiographic evaluation revealed Shone's complex associated with left ventricular non-compaction cardiomyopathy (NCC). To our knowledge, an association between NCC and Shone's complex has not been previously described.

摘要

肖恩综合征是一种罕见的先天性心脏畸形，其特征为左心在多个层面出现连续性梗阻性病变。本文描述了一例成年男性患者的特殊病例，该患者表现为心悸和进行性加重的呼吸困难。超声心动图评估显示肖恩综合征合并左心室致密化不全心肌病（NCC）。据我们所知，此前尚未有NCC与肖恩综合征之间关联的相关描述。