Wang Yu, Zhang Jiaqi, Feng Wei, Wu You, Yang Li, Yin Jiabao
Department of Ultrasound, Xiangyang No.1 People's Hospital, Hubei University of Medicine, Xiangyang, China.
Xiangyang Key Laboratory of Maternal-Fetal Medicine in Fetal Heart Disease, Xiangyang, China.
Echocardiography. 2019 Sep;36(9):1787-1789. doi: 10.1111/echo.14470. Epub 2019 Sep 5.
Unilateral absence of the pulmonary artery (UAPA) is a rare congenital cardiovascular malformation that can present as an isolated lesion or may be associated with other congenital heart malformations. Several studies have reported UAPA after birth. To our knowledge, the absence of the right pulmonary artery in the fetus has not been reported. Here, we report a rare case of fetal right pulmonary artery absence with aortic coarctation, which was confirmed by postpartum ultrasound and computed tomography angiography (CTA). Our case demonstrates that fetal echocardiography, especially the three-vessel view, is beneficial for the prenatal diagnosis of pulmonary artery malformations.
单侧肺动脉缺如（UAPA）是一种罕见的先天性心血管畸形，可表现为孤立性病变，也可能与其他先天性心脏畸形相关。已有多项研究报道了出生后的UAPA。据我们所知，胎儿右肺动脉缺如尚未见报道。在此，我们报告一例罕见的合并主动脉缩窄的胎儿右肺动脉缺如病例，产后超声和计算机断层血管造影（CTA）证实了这一情况。我们的病例表明，胎儿超声心动图，尤其是三血管切面，有助于肺动脉畸形的产前诊断。
