Flores Catalina, Lundberg Jaclyn, Richardson Randy R, Prasad Deepa
Phoenix Regional Campus, School of Medicine, Creighton University, Phoenix, AZ, USA.
Department of Radiology, St Joseph's Hospital and Medical Center, Phoenix, AZ, USA.
BMJ Case Rep. 2019 Sep 5;12(9):e230333. doi: 10.1136/bcr-2019-230333.
Primary cardiac tumours are relatively rare in the paediatric population, with benign tumours accounting for >90% of cases. Cardiac fibromas are rare primary tumours that typically reside in the ventricles. Symptoms are usually the result of blood outflow obstruction or disruption of the cardiac conduction system. They do not typically regress and usually require surgical intervention. In this case, we report a rare finding of a right atrial fibroma in an 18-month-old female who presented with lethargy and vomiting. Chest X-ray revealed an enlarged cardiac silhouette, and follow-up CT showed a 3.7×3.2×3.7 cm hypodense lesion in the right atrium. Cardiac MRI revealed the diagnosis, which was confirmed on pathology.
原发性心脏肿瘤在儿科人群中相对罕见,良性肿瘤占病例的90%以上。心脏纤维瘤是罕见的原发性肿瘤,通常位于心室。症状通常是血液流出受阻或心脏传导系统紊乱的结果。它们通常不会消退,通常需要手术干预。在本病例中,我们报告了一名18个月大的女性出现嗜睡和呕吐,罕见地发现右心房纤维瘤。胸部X线显示心脏轮廓增大,后续CT显示右心房有一个3.7×3.2×3.7厘米的低密度病变。心脏MRI确诊了该病,病理检查证实了诊断。