Moscoso Bosco, Congiu Stefano, Mayol Javier, Walter Carin, Caffarena José M
Department of Pediatric Cardiovascular Surgery, Hospital Sant Joan de Dèu, University of Barcelona, Barcelona, Spain.
Department of Pediatric Cardiology, Hospital Sant Joan de Dèu, University of Barcelona, Barcelona, Spain.
World J Pediatr Congenit Heart Surg. 2019 Sep;10(5):651-653. doi: 10.1177/2150135119867592.
Obstructive total anomalous pulmonary venous return (TAPVR) is a potentially life-threatening clinical condition and a surgical emergency. Left-sided partial anomalous pulmonary venous return (PAPVR) in association with a subdivided left atrium, also known as cor triatriatum sinister (CTS), is a very rare malformation that can mimic obstructive TAPVR. We present a case of a newborn with clinical manifestation of cardiogenic shock caused by CTS and PAPVR.
梗阻性完全性肺静脉异位引流(TAPVR)是一种潜在的危及生命的临床病症,也是一种外科急症。左侧部分性肺静脉异位引流(PAPVR)合并左心房分隔,也称为左心三房心(CTS),是一种非常罕见的畸形,可酷似梗阻性TAPVR。我们报告一例由CTS和PAPVR导致心源性休克临床表现的新生儿病例。