Huh Gene, Bae Yun Jung, Woo Hyun Jun, Park Jung Hyun, Koo Ja-Won, Song Jae-Jin
Department of Otorhinolaryngology-Head and Neck Surgery, Seoul National University Bundang Hospital, Seongnam, Korea.
Department of Radiology, Seoul National University Bundang Hospital, Seongnam, Korea.
Clin Exp Otorhinolaryngol. 2020 May;13(2):123-132. doi: 10.21053/ceo.2019.00780. Epub 2019 Sep 17.
Vertebrobasilar dolichoectasia (VBD), an elongation and distension of vertebrobasilar artery, may present with cranial nerve symptoms due to nerve root compression. The objectives of this study are to summarize vestibulocochlear manifestations in subjects with VBD through a case series and to discuss the needs of thorough oto-neurotologic evaluation in VBD subjects before selecting treatment modalities.
Four VBD subjects with vestibulocochlear manifestations were reviewed retrospectively. VBD was confirmed by either brain or internal auditory canal magnetic resonance imaging (MRI) and magnetic resonance angiography (MRA). Patient information, medical history, MRI/MRA findings, and audiometry or vestibular function tests were reviewed according to patient's specific symptom.
Of the four subjects, three presented with ipsilesional sensorineural hearing loss (SNHL), three with paroxysmal recurrent vertigo, and two with typewriter tinnitus. The MRI/MRA of the four subjects revealed unilateral VBD with neurovascular compression of cisternal segment or the brainstem causing displacement, angulation, or deformity of the cranial nerve VII or VIII that corresponded to the symptoms.
Vestibulocochlear symptoms such as SNHL, recurrent paroxysmal vertigo, or typewriter tinnitus can be precipitated from a neurovascular compression of the vestibulocochlear nerve by VBD. Because proper medical or surgical treatments may stop the disease progression or improve audio-vestibular symptoms in subjects with VBD, a high index of suspicion and meticulous radiologic evaluation are needed when vestibulocochlear symptoms are not otherwise explainable, and if VBD is confirmed to cause audiovestibular manifestation, a thorough oto-neurotologic evaluation should be performed before initial treatment.
椎基底动脉延长扩张症(VBD)是椎基底动脉的延长和扩张,可因神经根受压而出现颅神经症状。本研究的目的是通过一系列病例总结VBD患者的前庭蜗神经表现,并讨论在选择治疗方式之前对VBD患者进行全面耳神经学评估的必要性。
回顾性分析4例有前庭蜗神经表现的VBD患者。通过脑部或内耳道磁共振成像(MRI)及磁共振血管造影(MRA)确诊VBD。根据患者的具体症状,回顾患者信息、病史、MRI/MRA检查结果以及听力测定或前庭功能测试结果。
4例患者中,3例出现同侧感音神经性听力损失(SNHL),3例出现阵发性复发性眩晕,2例出现打字机样耳鸣。4例患者的MRI/MRA显示单侧VBD,伴有脑池段或脑干的神经血管压迫,导致与症状相对应的面神经VII或前庭蜗神经VIII移位、成角或畸形。
VBD导致的前庭蜗神经血管压迫可引发SNHL、复发性阵发性眩晕或打字机样耳鸣等前庭蜗神经症状。由于适当的内科或外科治疗可能会阻止VBD患者的疾病进展或改善听觉前庭症状,因此,当前庭蜗神经症状无法用其他原因解释时,需要高度怀疑并进行细致的影像学评估;如果确诊VBD导致听觉前庭表现,则应在初始治疗前进行全面的耳神经学评估。