脊髓小脑共济失调17型中的自伤行为：一项新的临床观察
Self-Injurious Behaviour in SCA17: A New Clinical Observation.
作者信息
Bonomo Roberta, Latorre Anna, Bhatia Kailash P
机构信息
Department of Clinical and Movement Neurosciences, University College London (UCL) Institute of Neurology, London, UK.
Department "G.F. Ingrassia", Section of Neurosciences, University of Catania, Catania, IT.
出版信息
Tremor Other Hyperkinet Mov (N Y). 2019 Sep 5;9. doi: 10.7916/tohm.v0.672. eCollection 2019.
BACKGROUND
Self-injurious behaviour has historically been associated with borderline personality disorder. Nevertheless, over recent years, it has been reported in numerous neurological syndromes, especially hyperkinesias.
CASE REPORT
Two cases of SCA17 manifested self-injurious behaviour, namely repetitive scratching of the skin resulting in severe excoriations. In one of them, the abnormal behaviour was associated with the inability to resist the impulse to commit the act along with relief following the damage.
DISCUSSION
This is the first report describing self-injurious behaviour in SCA17, but the mechanisms underlying it are still not clear. Further studies are needed to clarify the pathophysiology of such manifestation in hyperkinetic syndromes.
背景
自伤行为在历史上一直与边缘型人格障碍相关联。然而，近年来，在许多神经综合征中都有报道，尤其是运动亢进。
病例报告
两例SCA17患者表现出自伤行为，即反复抓挠皮肤导致严重擦伤。其中一例中，异常行为与无法抗拒实施该行为的冲动以及损伤后的缓解有关。
讨论
这是第一份描述SCA17患者自伤行为的报告，但其潜在机制仍不清楚。需要进一步研究以阐明运动亢进综合征中这种表现的病理生理学。
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