Sedaghat Mohammad-Reza, Momeni-Moghaddam Hamed, Haghighi Batool, Moshirfar Majid
Eye Research Center, Mashhad University of Medical Sciences, Mashhad.
Health Promotion Research Center, Zahedan University of Medical Sciences, Zahedan.
Medicine (Baltimore). 2019 Sep;98(39):e17054. doi: 10.1097/MD.0000000000017054.
To report the visual status and results of phacoemulsification cataract surgery in a young patient with Alport syndrome associated with bilateral anterior lenticonus. The milestone of this report is the use of anterior segment optical coherence tomography (AS-OCT) to confirm the central protrusion of the anterior surface of the crystalline lens.
A 23-year-old young woman presented with severe progressive visual loss in both eyes, which started several years ago.
Refractive status was indicative of high myopia with astigmatism and vision was not improved with optimal correction to better than 0.1 in the right eye and 0.2 in the left eye (visual acuities given in decimal notation). Slit-lamp examination showed transparent cornea, anterior lenticonus and posterior sub-capsular cataract in both eyes. The classical appearance of oil droplet was evident using retro-illumination on the slit lamp.
The natural lenses were replaced with intraocular lens (IOL).
An excellent refractive status achieved associated with an uncorrected distance visual acuity 0.9 and 0.8 in the right and left eye, respectively.
AS-OCT is a valuable device for confirming the budging of the anterior crystalline lens surface.
报告一名患有阿尔波特综合征并伴有双侧前圆锥形晶状体的年轻患者的视力状况及白内障超声乳化手术结果。本报告的关键在于使用眼前节光学相干断层扫描（AS-OCT）来确认晶状体前表面的中央突出。
一名23岁年轻女性，双眼出现严重进行性视力丧失，始于数年前。
屈光状态显示为高度近视合并散光，最佳矫正后右眼视力未提高至0.1以上，左眼视力未提高至0.2以上（视力以小数记录法给出）。裂隙灯检查显示双眼角膜透明、前圆锥形晶状体和后囊下白内障。在裂隙灯上使用后照法时，典型的油滴样外观明显。
将自然晶状体替换为人工晶状体（IOL）。
获得了极佳的屈光状态，右眼和左眼的未矫正远视力分别为0.9和0.8。
AS-OCT是确认晶状体前表面突出的一种有价值的设备。
