Department of Radiation Oncology.
Division of Neurosurgery, and.
J Natl Compr Canc Netw. 2019 Oct 1;17(10):1148-1153. doi: 10.6004/jnccn.2019.7336.
Primary melanoma of the pineal gland is a rare disease entity with an overall poor prognosis. Limited data exist to appropriately guide treatment decisions. Historical case reports have showed some success using a combination of surgical resection, radiotherapy, and chemotherapy, but long-term survival has been exceedingly rare. This report presents a female patient with a primary pineal melanoma who underwent subtotal resection followed by adjuvant focal radiation to the residual tumor. Immunohistochemistry identified a strong positivity for PD-L1 (70%). After radiation, systemic therapy with pembrolizumab was initiated with the plan to treat until progression. She has now completed 33 cycles of pembrolizumab without interruptions, complications, or disease progression. At the time of writing, the patient has had an excellent clinical outcome, with a durable near-complete response of >138 weeks. To our knowledge, this is the first patient with a pineal melanoma to be managed by targeting PD-L1. Furthermore, she has achieved the second longest overall survival and the longest progression-free survival reported in the literature.
松果体原发性黑色素瘤是一种罕见的疾病实体,总体预后较差。目前的数据有限,无法为治疗决策提供适当的指导。历史病例报告显示,手术切除、放疗和化疗联合使用有一定疗效,但长期生存极为罕见。本报告介绍了一例女性松果体原发性黑色素瘤患者,行肿瘤次全切除术,术后残余肿瘤行辅助局部放疗。免疫组化显示 PD-L1 强阳性(70%)。放疗后,给予 pembrolizumab 系统治疗,计划进行治疗直至疾病进展。目前,患者已完成 33 个周期的 pembrolizumab 治疗,无中断、并发症或疾病进展。在撰写本文时,患者的临床结局极好,持续的近完全缓解超过 138 周。据我们所知,这是首例采用 PD-L1 靶向治疗的松果体黑色素瘤患者。此外,她的总生存期和无进展生存期均为文献报道中第二长和最长。