Almubarak Abdulaziz Oqalaa, Ulhaq Anwar, BinDahmash Abdulmajeed, Al Shail Essam
Division of Neurosurgery, Neurosciences Department, King Faisal Specialist Hospital and Research Center, Riyadh, Saudi Arabia,
Department of Neurosurgery, Prince Mohammed Medical City, Riyadh, Saudi Arabia,
Pediatr Neurosurg. 2019;54(6):399-404. doi: 10.1159/000502615. Epub 2019 Oct 8.
Pilomyxoid astrocytoma (PMA) is a rare brain tumour generally located in the chiasmatic-hypothalamic region. In comparison to pilocytic astrocytoma, PMA has distinct histopathological features, aggressive clinical behaviour, a high recurrence rate, and early cerebrospinal fluid dissemination. Only 14 cases of PMA have been reported in the spinal cord since its pathological description in 1999. Here, we report the 15th case in a 3-year-old girl who was treated with chemoradiotherapy and followed up for 5 years. In this report, we also present a review of spinal PMA including treatment options and prognosis.
毛黏液样星形细胞瘤（PMA）是一种罕见的脑肿瘤，通常位于视交叉 - 下丘脑区域。与毛细胞型星形细胞瘤相比，PMA具有独特的组织病理学特征、侵袭性的临床行为、高复发率以及早期脑脊液播散。自1999年其病理描述以来，脊髓中仅报告了14例PMA。在此，我们报告第15例，患者为一名3岁女孩，接受了放化疗并随访5年。在本报告中，我们还对脊髓PMA进行了综述，包括治疗选择和预后。
