Drack G, Baumann H, Lauper U, Huch A, Hirzel H O
Klinik und Poliklinik für Geburtshilfe, Universitätsspital Zürich.
Schweiz Med Wochenschr. 1988 Jul 30;118(30):1110-2.
Ebstein's anomaly is characterized by abnormalities both in the basal and in the free attachments of the leaflets of the tricuspid valve. Fairly frequently the developmental defect is associated with a WPW syndrome (Type B). The main obstetric problems arise from tachyarrhythmias. Since tachycardias in these patients are due to physical stress, correct planning of delivery calls for lightening of the hemodynamic burden of labor, careful analysis of the cardiac status, meticulous preparation for optimum antiarrhythmic therapy and correct timing for induction of labor. The case of a young primipara with Ebstein's anomaly is presented to typify the need for cooperation of subspecialities.
埃布斯坦畸形的特征是三尖瓣叶基底部和游离附着部均存在异常。这种发育缺陷相当频繁地与WPW综合征(B型)相关联。主要的产科问题源于快速性心律失常。由于这些患者的快速性心律失常是由身体应激引起的,因此正确的分娩计划需要减轻分娩时的血流动力学负担、仔细分析心脏状况、精心准备最佳抗心律失常治疗以及正确把握引产时机。现介绍一名患有埃布斯坦畸形的年轻初产妇病例,以体现各专科合作的必要性。