Martina B, Marincek B
Medizinische Universitätsklinik, Inselspital Bern.
Schweiz Med Wochenschr. 1988 Aug 27;118(34):1213-6.
A patient with an inflammatory fibrous tumor of the mesenteric fat tissue is reported. Clinical signs were epigastric pain, weight loss and palpable abdominal mass. diagnosis was by abdominal CT and surgical biopsy. The histological feature was diffuse fibrosis. Isolated mesenteric fibrosis is a rare variety of systemic idiopathic fibrosis, a disease entity including fibrosis of the retroperitoneum and other sites. Among possible etiological factors an autoimmune origin, drugs (methysergide) and lymphatic obstruction are discussed. Our patient had congenital hypoplasia of the lymphatic drainage system of the legs. She recovered rapidly and spontaneously and the tumor regressed on CT. Fatal courses are exceptional and medical therapy usually is not required.
报告了一名患有肠系膜脂肪组织炎性纤维瘤的患者。临床症状为上腹部疼痛、体重减轻和可触及的腹部肿块。通过腹部CT和手术活检进行诊断。组织学特征为弥漫性纤维化。孤立性肠系膜纤维化是系统性特发性纤维化的一种罕见类型，系统性特发性纤维化是一种包括腹膜后和其他部位纤维化的疾病实体。在可能的病因中，讨论了自身免疫起源、药物（麦角新碱）和淋巴阻塞。我们的患者有腿部淋巴引流系统先天性发育不全。她迅速自发康复，肿瘤在CT上消退。致命病程罕见，通常不需要药物治疗。
