Seibert D A, Terry J E
Eye Clinic, VA Medical Center, Huntington, WV 25704.
J Am Optom Assoc. 1988 Oct;59(10):798-801.
Foveomacular vitelliform degeneration, adult type (FVDAT) is a disciform, macular degeneration that is usually encountered in the fifth to seventh decade of life. It appears ophthalmoscopically similar to the vitelliform or "egg-yolk" stage of Best's disease (vitelliform degeneration), but shows no inheritance pattern. Electrooculographic (EOG) testing reveals a normal or only slightly reduced Arden ratio (light peak/dark trough). The prognosis is optimistic, as most patients retain reading vision throughout life. This case report describes an atypical case in which the signs and symptoms of FVDAT are not exactly those regularly seen. However, it does closely resemble the disease sufficiently to warrant this diagnosis.
成人型黄斑中心凹卵黄样变性(FVDAT)是一种盘状黄斑变性,通常发生在50至70岁之间。在检眼镜下,它看起来与Best病(卵黄样变性)的卵黄样或“蛋黄”阶段相似,但没有遗传模式。眼电图(EOG)测试显示Arden比值(光峰/暗谷)正常或仅略有降低。预后乐观,因为大多数患者终生保留阅读视力。本病例报告描述了一例非典型病例,其中FVDAT的体征和症状并不完全是常见的表现。然而,它与该疾病的相似性足以支持这一诊断。