Picón Jaimes Yelson Alejandro, Orozco Chinome Javier Esteban, Molina-Franky Jessica
Universidad Pedro de Valdivia.
Rev Fac Cien Med Univ Nac Cordoba. 2019 Dec 11;76(4):257-260. doi: 10.31053/1853.0605.v76.n4.24963.
The Achenbach syndrome was described in the '50s by the German physician Walter Achenbach and corresponds to an entity characterized by the appearance of ecchymosis or purpura and even bruises on the fingers and sometimes on the feet. It courses benignly and is self-limited.
We present the case of a 60-year-old woman who was diagnosed with this syndrome after performing laboratory tests, antibodies and images without finding alterations in them, with improvement after receiving analgesia and physical means.
The Achenbach syndrome continues to be an unknown entity, with few reports in the literature. Up to the year 2 016, 12 case reports had been identified worldwide, concluding that it is a pathology that mainly affects women between the fifth and sixth decade of life.
Although this nosological entity is benign and its pathophysiology is not entirely clear, it is important that during the initial approach it is consulted for similar episodes in the past and if it is an acute event, look for other alterations such as delay in capillary refill, coldness distal, absence of pulses and thus discarding acute ischemic pathology with diagnostic exams.
阿肯巴克综合征由德国医生沃尔特·阿肯巴克在20世纪50年代描述,是一种以手指甚至有时足部出现瘀斑、紫癜甚至瘀伤为特征的病症。其病程呈良性且具有自限性。
我们报告一例60岁女性病例,该患者经实验室检查、抗体检测及影像学检查后被诊断为此综合征,检查未发现异常,接受镇痛治疗及物理治疗后病情好转。
阿肯巴克综合征仍是一种不明病症,文献报道较少。截至2016年,全球共识别出12例病例报告,结论是该病症主要影响50至60岁的女性。
尽管此病症实体为良性且其病理生理学尚不完全清楚,但在初始诊疗过程中,询问既往类似发作情况很重要,如果是急性事件,要查找其他异常,如毛细血管再充盈延迟、远端发冷、无脉搏等,从而通过诊断检查排除急性缺血性病变。