Jahanimoghadam Fatemeh, Sharifi Maryam
Oral and Dental Diseases Research Center, Kerman Social Determinants on Oral Health Research Center, Dept. of Pediatric Dentistry, School of Dentistry, Kerman University of Medical Sciences, Kerman, Iran.
Resident Dept. of Pediatric Dentistry, School of Dentistry, Kerman University of Medical Sciences, Kerman, Iran.
J Dent (Shiraz). 2019 Dec;20(4):298-303. doi: 10.30476/DENTJODS.2019.44905.
Goldenhar syndrome (GHS) is a complex syndrome characterized by relation of mandibular hypoplasia, abnormality of the ear, ocular dermoid and vertebral disorders and hemi facial macrosomia. Treatment protocol depends on the patient's age and systemic clinical presentations, with a multidisciplinary method often being required. This case report describes a typical 6-year-old female patient who presented to the Department of Pediatric Dentistry, Faculty of Dentistry, University of Medical Sciences, Kerman, Iran with mandibular hypoplasia, facial asymmetry, ear tags and ocular dermoid after plastic surgery. Diagnosis was based on clinical aspects, radiology and laboratory findings. GHS is a developmental complaint that can disturb many aspects of the patient's life; therefore, immediate treatment from birth is necessary.
戈尔登哈综合征(GHS)是一种复杂的综合征,其特征为下颌发育不全、耳部异常、眼皮样囊肿、脊柱疾病以及半侧颜面巨大症。治疗方案取决于患者的年龄和全身临床表现,通常需要多学科方法。本病例报告描述了一名典型的6岁女性患者,她因下颌发育不全、面部不对称、耳赘和眼皮样囊肿在接受整形手术后就诊于伊朗克尔曼医科大学牙科学院儿童牙科。诊断基于临床症状、放射学和实验室检查结果。戈尔登哈综合征是一种发育性疾病,会干扰患者生活的许多方面;因此,从出生起就需要立即进行治疗。