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缩窄性心包炎和限制型心肌病的血液动力学。

Hemodynamics of constrictive pericarditis and restrictive cardiomyopathy.

机构信息

Department of Cardiovascular Medicine, William Beaumont Hospital, Royal Oak, Michigan.

Veterans Administration Long Beach Health Care System, University of California, Irvine, California.

出版信息

Catheter Cardiovasc Interv. 2020 May 1;95(6):1240-1248. doi: 10.1002/ccd.28692. Epub 2020 Jan 6.

DOI:10.1002/ccd.28692
PMID:31904891
Abstract

Constrictive pericarditis (CP) and restrictive cardiomyopathy (RCM) are indolent disabling diseases of diastolic function. The two conditions share common pathophysiologic features, resulting in similar and overlapping clinical presentations, echocardiographic findings, and hemodynamic characteristics. However, their clinical course differs, as CP is surgically curable whereas RCM is a chronic condition managed medically. Separating these two entities is based on delineation of anatomic and physiologic derangements employing multimodality hemodynamic interrogation by advanced imaging techniques (Echo-Doppler, CT, and especially MRI) combined with sophisticated invasive hemodynamics.

摘要

缩窄性心包炎(CP)和限制型心肌病(RCM)是两种惰性的舒张功能障碍性疾病。这两种疾病具有共同的病理生理特征,导致相似和重叠的临床表现、超声心动图表现和血流动力学特征。然而,它们的临床病程不同,因为 CP 可以通过手术治愈,而 RCM 是一种慢性疾病,需要药物治疗。通过先进的影像学技术(超声心动图、CT,尤其是 MRI)结合复杂的有创血流动力学检查,对解剖和生理异常进行多模态血流动力学评估,可以将这两种疾病区分开来。

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