肺尖原发性透明细胞肉瘤伴脊柱转移：致命结局。
Primary clear cell sarcoma in the lung apex with spinal metastasis: a fatal outcome.
作者信息
Sass RemyGrace, Tandra Pavan Kumar, Shonka Nicole, Manzer Melissa
机构信息
College of Medicine, University of Nebraska Medical Center, Omaha, Nebraska, USA.
Hematology-Oncology, University of Nebraska Medical Center, Omaha, Nebraska, USA
出版信息
BMJ Case Rep. 2020 Jan 9;13(1):e231556. doi: 10.1136/bcr-2019-231556.
Clear cell sarcoma (CCS) is a rare tumour that manifests in tendons and aponeuroses of the distal extremities and comprises roughly 1% of all soft tissue cancers. Only two cases of a primary CCS arising in the lung have been reported in the literature, and neither were located in the lung apex. We report a case of a primary CCS located in the lung apex that originally presented as ptosis, as well as arm pain and weakness. Distant metastasis was discovered on diagnosis, which led to irreversible paraplegia and death of the patient.
透明细胞肉瘤（CCS）是一种罕见的肿瘤，表现于远端肢体的肌腱和腱膜，约占所有软组织癌的1%。文献中仅报道过两例原发于肺部的CCS病例，且均不在肺尖。我们报告一例原发于肺尖的CCS病例，最初表现为上睑下垂以及手臂疼痛和无力。诊断时发现有远处转移，导致患者出现不可逆的截瘫并死亡。
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