Kazakos Constantinos J, Galanis Vasilios G, Giatromanolaki Alexandra, Verettas Dennis-Alexander J, Sivridis Efthimios
Department of Orthopedics, University Hospital of Alexandroupolis, Democritus University of Thrace, Alexandroupolis, Greece.
World J Surg Oncol. 2006 Aug 7;4:48. doi: 10.1186/1477-7819-4-48.
Clear cell sarcoma of tendons and aponeuroses (CCSTA) appears usually in the extremities and rarely in the trunk.
We present an unusual case of CCSTA overlying the scapular region and with secondary osseous extension in the lower scapula. The patient underwent a wide local excision with removal of the tumor and the lower two thirds of the scapula. He had no local recurrences but he developed lung metastases after 5 months in spite of postoperative chemotherapy. He finally died ten months later.
The patients with CCSTA have a variable unpredictable course. Despite treatment the overall prognosis is poor.
腱膜透明细胞肉瘤(CCSTA)通常出现在四肢,很少出现在躯干。
我们报告一例罕见的CCSTA病例,肿瘤位于肩胛区域并继发于肩胛骨下部骨质浸润。患者接受了广泛的局部切除,切除了肿瘤及肩胛骨下三分之二。患者无局部复发,但尽管术后进行了化疗,5个月后仍出现肺转移。10个月后患者最终死亡。
CCSTA患者的病程多变且难以预测。尽管进行了治疗,但总体预后较差。