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镰状细胞病:初级保健更新。

Sickle cell disease: A primary care update.

机构信息

Department of Pediatrics, The Metrohealth Hospital, and Assistant Professor, Case Western Reserve University, Cleveland, OH.

Department of Pediatric Hematology and Oncology and Blood and Marrow Transplant Program, Cleveland Clinic; Assistant Professor, Cleveland Clinic Lerner College of Medicine of Case Western Reserve University, Cleveland, OH

出版信息

Cleve Clin J Med. 2020 Jan;87(1):19-27. doi: 10.3949/ccjm.87a.18051. Epub 2020 Jan 2.

DOI:10.3949/ccjm.87a.18051
PMID:31990651
Abstract

Sickle cell disease (SCD) is the most common hemoglobinopathy in the United States and causes significant disease-related morbidity including multiorgan damage, chronic anemia, and debilitating pain crises. Primary care physicians play a key role in the medical home model of care for adults with SCD. This review focuses on current recommendations for health maintenance and provides a brief summary of disease complications and current updates.

摘要

镰状细胞病(SCD)是美国最常见的血红蛋白病,可导致多器官损伤、慢性贫血和使人虚弱的疼痛危象等严重的与疾病相关的发病率。初级保健医生在 SCD 成人的医疗之家护理模式中发挥着关键作用。本综述重点介绍了目前的健康维护建议,并简要总结了疾病并发症和最新进展。

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