Department of Immunology, Guangxi Area of Excellence, Guilin Medical University, Guilin, China.
Center for Systems Medicine, Guangxi Key Laboratory of Excellence, Guilin Medical University, Guilin, China.
Front Immunol. 2020 Jan 9;10:2980. doi: 10.3389/fimmu.2019.02980. eCollection 2019.
Amyloid deposition is a histological hallmark of common human disorders including Alzheimer's disease (AD) and type 2 diabetes. Although some reports highlight that amyloid fibrils might activate the innate immunity system via pattern recognition receptors, here, we provide multiple lines of evidence for the protection by site-specific amyloid protein analogs and fibrils against autoimmune attacks: (1) strategies targeting clearance of the AD-related brain amyloid plaque induce high risk of deadly autoimmune destructions in subjects with cognitive dysfunction; (2) administration of amyloidogenic peptides with either full length or core hexapeptide structure consistently ameliorates signs of experimental autoimmune encephalomyelitis; (3) experimental autoimmune encephalomyelitis is exacerbated following genetic deletion of amyloid precursor proteins; (4) absence of islet amyloid coexists with T-cell-mediated insulitis in autoimmune diabetes and autoimmune polyendocrine syndrome; (5) use of islet amyloid polypeptide agonists rather than antagonists improves diabetes care; and (6) common suppressive signaling pathways by regulatory T cells are activated in both local and systemic amyloidosis. These findings indicate dual modulation activity mediated by amyloid protein monomers, oligomers, and fibrils to maintain immune homeostasis. The protection from autoimmune destruction by amyloid proteins offers a novel therapeutic approach to regenerative medicine for common degenerative diseases.
淀粉样沉积是包括阿尔茨海默病(AD)和 2 型糖尿病在内的常见人类疾病的组织学标志。虽然有一些报道强调淀粉样纤维可能通过模式识别受体激活先天免疫系统,但在这里,我们提供了多条证据表明,特定部位的淀粉样蛋白类似物和纤维对自身免疫攻击具有保护作用:(1)针对清除与 AD 相关的脑淀粉样斑块的策略会增加认知功能障碍患者发生致命自身免疫破坏的风险;(2)全长或核心六肽结构的淀粉样肽给药一致改善实验性自身免疫性脑脊髓炎的症状;(3)淀粉样前体蛋白基因缺失会加剧实验性自身免疫性脑脊髓炎;(4)胰岛淀粉样共存与自身免疫性糖尿病和自身免疫性多内分泌综合征中的 T 细胞介导的胰岛炎;(5)使用胰岛淀粉样多肽激动剂而不是拮抗剂可改善糖尿病治疗;(6)在局部和系统性淀粉样变性中,调节性 T 细胞的常见抑制信号通路被激活。这些发现表明,淀粉样蛋白单体、寡聚体和纤维介导的双重调节活性可维持免疫稳态。淀粉样蛋白对自身免疫破坏的保护为常见退行性疾病的再生医学提供了一种新的治疗方法。