Department of Medicine, The Ohio State University College of Medicine, Columbus, Ohio, USA .
Department of Medicine, University of Pittsburgh, Pittsburgh, Pennsylvania, USA.
JCI Insight. 2020 Jan 30;5(2):125895. doi: 10.1172/jci.insight.125895.
Our integrative genomic and functional analysis identified transforming acidic coiled-coil-containing protein 2 (TACC2) as a chronic obstructive pulmonary disease (COPD) candidate gene. Here, we found that smokers with COPD exhibit a marked decrease in lung TACC2 protein levels relative to smokers without COPD. Single cell RNA sequencing reveals that TACC2 is expressed primarily in lung epithelial cells in normal human lungs. Furthermore, suppression of TACC2 expression impairs the efficiency of homologous recombination repair and augments spontaneous and cigarette smoke extract-induced (CSE-induced) DNA damage and cytotoxicity in immortalized human bronchial epithelial cells. By contrast, enforced expression of TACC2 attenuates the CSE effects. We also found that CSE enhances TACC2 degradation via the ubiquitin-proteasome system mediated by the ubiquitin E3 ligase subunit, F box L7. Furthermore, cellularly expressed TACC2 proteins harboring naturally occurring mutations exhibited altered protein lifespan coupled with modified DNA damage repair and cytotoxic responses. CS triggers emphysematous changes accompanied by accumulated DNA damage, apoptosis of alveolar epithelia, and lung inflammation in Tacc2-/- compared with Tacc2+/+ mice. Our results suggest that CS destabilizes TACC2 protein in lung epithelia by the ubiquitin proteasome system, leading to subsequent DNA damage, cytotoxicity, and emphysema.
我们的综合基因组和功能分析确定转化酸性卷曲螺旋蛋白 2(TACC2)是慢性阻塞性肺疾病(COPD)的候选基因。在这里,我们发现 COPD 吸烟者的肺 TACC2 蛋白水平明显低于非 COPD 吸烟者。单细胞 RNA 测序显示,TACC2 在正常人类肺中的肺上皮细胞中主要表达。此外,抑制 TACC2 表达会损害同源重组修复的效率,并增强永生化人支气管上皮细胞中自发和香烟烟雾提取物(CSE 诱导)引起的 DNA 损伤和细胞毒性。相比之下,强制表达 TACC2 可减轻 CSE 的影响。我们还发现 CSE 通过泛素 E3 连接酶亚基 F 框 L7 介导的泛素蛋白酶体系统增强 TACC2 降解。此外,表达细胞内的 TACC2 蛋白携带天然存在的突变,其表现出改变的蛋白寿命,以及修饰的 DNA 损伤修复和细胞毒性反应。CS 引发肺气肿变化,伴有肺泡上皮细胞的累积 DNA 损伤、凋亡和 Tacc2-/-小鼠中的肺部炎症,与 Tacc2+/+小鼠相比。我们的结果表明,CS 通过泛素蛋白酶体系统使肺上皮细胞中的 TACC2 蛋白不稳定,导致随后的 DNA 损伤、细胞毒性和肺气肿。