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尼泊尔首例克雅氏病报告病例。

The first reported case of Creutzfeldt-Jakob disease from Nepal.

作者信息

Kharel Himal, Adhikari Pabitra, Pokhrel Nishan B, Kharel Zeni, Nepal Gaurav

机构信息

Tribhuvan University Institute of Medicine Kathmandu Nepal.

Department of Internal Medicine Rochester General Hospital Rochester NY USA.

出版信息

Clin Case Rep. 2019 Dec 12;8(1):198-202. doi: 10.1002/ccr3.2609. eCollection 2020 Jan.

DOI:10.1002/ccr3.2609
PMID:31998516
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6982523/
Abstract

Creutzfeldt-Jakob disease (CJD) can also be diagnosed in a resource-limited setting through good clinical analysis. The diagnosis of CJD should be considered in patients with rapidly evolving neurological signs associated with cognitive disturbances even in countries with limited available sophisticated tools and where CJD was never reported before.

摘要

克雅氏病(CJD)也可在资源有限的情况下,通过良好的临床分析进行诊断。即使在拥有先进工具有限且此前从未报告过克雅氏病的国家,对于出现与认知障碍相关的快速进展性神经体征的患者,也应考虑克雅氏病的诊断。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12e6/6982523/44ebd9b5c5a3/CCR3-8-198-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12e6/6982523/19c2dc4d31bb/CCR3-8-198-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12e6/6982523/44ebd9b5c5a3/CCR3-8-198-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12e6/6982523/19c2dc4d31bb/CCR3-8-198-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/12e6/6982523/44ebd9b5c5a3/CCR3-8-198-g002.jpg

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本文引用的文献

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Differential diagnosis with other rapid progressive dementias in human prion diseases.人类朊病毒病与其他快速进展性痴呆的鉴别诊断。
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Neuropsychological Symptoms in Sporadic Creutzfeldt-Jakob Disease Patients in Germany.德国散发性克雅氏病患者的神经心理学症状
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A rare case of Creutzfeldt-Jakob disease reported from Nepal.尼泊尔报告的一例罕见克雅氏病病例。
Clin Case Rep. 2021 Sep 13;9(9):e04804. doi: 10.1002/ccr3.4804. eCollection 2021 Sep.
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Sporadic Creutzfeldt-Jakob disease: A case report and review of literature.散发性克雅氏病:一例病例报告及文献综述
Clin Case Rep. 2020 Jul 16;8(11):2240-2244. doi: 10.1002/ccr3.3131. eCollection 2020 Nov.
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Imaging of Creutzfeldt-Jakob Disease: Imaging Patterns and Their Differential Diagnosis.克雅氏病的影像学表现:影像模式及其鉴别诊断
Radiographics. 2017 Jan-Feb;37(1):234-257. doi: 10.1148/rg.2017160075.
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Cerebrospinal fluid real-time quaking-induced conversion is a robust and reliable test for sporadic creutzfeldt-jakob disease: An international study.脑脊液实时震颤诱导转化检测是散发性克雅氏病的一种强大且可靠的检测方法:一项国际研究。
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The Diagnosis and Treatment of Autoimmune Encephalitis.自身免疫性脑炎的诊断与治疗
J Clin Neurol. 2016 Jan;12(1):1-13. doi: 10.3988/jcn.2016.12.1.1.
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Prion Diseases.朊病毒疾病
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Comparing CSF biomarkers and brain MRI in the diagnosis of sporadic Creutzfeldt-Jakob disease.比较脑脊液生物标志物和脑部磁共振成像在散发性克雅氏病诊断中的作用。
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The different faces of Creutzfeldt-Jacob disease CJD in psychiatry.
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Behavioral and psychiatric symptoms in prion disease.朊病毒病的行为和精神症状。
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