Hajjar R, Plasse M, Vandenbroucke-Menu F, Schwenter F, Sebajang H
Centre hospitalier de l'Université de Montréal, Canada.
Ann R Coll Surg Engl. 2020 Apr;102(4):e1-e3. doi: 10.1308/rcsann.2020.0010. Epub 2020 Jan 31.
Solid pseudopapillary tumours of the pancreas and giant splenic cysts are very rare entities, and their coexistence in a young female patient has not been previously reported in the literature. We present the case of a 27-year-old woman who presented with abdominal pain and two masses on abdominal imaging. A mass located in the right upper quadrant was biopsied, and histological and immunohistochemical analysis showed a solid pseudopapillary tumour of the pancreas. A giant cystic splenic lesion was also noted. The patient underwent a distal pancreatectomy and splenectomy in our referral centre. Margins were negative on histopathological examination. Negative surgical margins were achieved with distal pancreatectomy and splenectomy despite the large size of the pancreatic tumour. The management of solid pseudopapillary tumours of the pancreas is often challenging and the concomitant presence of a giant splenic cyst poses additional challenges to the surgical management of such tumours.
胰腺实性假乳头状肿瘤和巨大脾囊肿是非常罕见的疾病，它们在年轻女性患者中共存的情况此前在文献中尚无报道。我们报告一例27岁女性患者，其因腹痛就诊，腹部影像学检查发现两个肿块。对位于右上腹的一个肿块进行活检，组织学和免疫组化分析显示为胰腺实性假乳头状肿瘤。同时还发现了一个巨大的脾囊肿性病变。该患者在我们的转诊中心接受了胰体尾切除术和脾切除术。组织病理学检查切缘阴性。尽管胰腺肿瘤体积较大，但通过胰体尾切除术和脾切除术实现了阴性手术切缘。胰腺实性假乳头状肿瘤的治疗通常具有挑战性，而巨大脾囊肿的并存给此类肿瘤的手术治疗带来了额外的挑战。
