Chai Victor, Fox Adrian, Chong Lynn, House Eloise, Sutherland Tom
Upper Gastrointestinal and Hepatobiliary Surgical Unit, St Vincent's Hospital Melbourne, Fitzroy, Victoria, Australia.
Upper Gastrointestinal and Hepatobiliary Surgical Unit, Eastern Health, Fitzroy, Victoria, Australia.
J Clin Ultrasound. 2020 Jun;48(5):283-286. doi: 10.1002/jcu.22819. Epub 2020 Feb 3.
Epithelioid hepatic angiomyolipoma (Epi-HAML) is a rare hepatic tumor frequently misdiagnosed as hepatocellular carcinoma (HCC). Unlike conventional angiomyolipoma (AML), Epi-HAML contains minimal amount of adipose tissue, which is a radiological distinguishing feature between AML and HCC. Two patients were referred for management of incidentally found hepatic lesions confirmed to be Epi-HAML on post-resection tissue analysis. CT and MRI findings were suggestive of HCC. Contrast-enhanced ultrasound demonstrated intratumoral shunting, a feeding artery, and early draining hepatic vein. These findings should alert radiologists to the possibility of Epi-HAML. Furthermore, these features may be better assessed by contrast-enhanced ultrasound due to its superior dynamic temporal resolution.
上皮样肝血管平滑肌脂肪瘤（Epi-HAML）是一种罕见的肝脏肿瘤，常被误诊为肝细胞癌（HCC）。与传统血管平滑肌脂肪瘤（AML）不同，Epi-HAML含极少脂肪组织，这是AML与HCC之间的一个影像学鉴别特征。两名患者因偶然发现的肝脏病变前来就诊，术后组织分析证实为Epi-HAML。CT和MRI表现提示为HCC。超声造影显示瘤内分流、供血动脉和早期引流肝静脉。这些发现应提醒放射科医生注意Epi-HAML的可能性。此外，由于超声造影具有 superior动态时间分辨率，这些特征可能通过超声造影得到更好的评估。
