孤立性颅内 Rosai-Dorfman 病：病例报告及文献复习。
Isolated Intracranial Rosai-Dorfman Disease: Case Report and Review of the Literature.
机构信息
Department of Neurosurgery, University Hospitals Plymouth NHS Trust, Plymouth, England; Department of Cellular & Anatomical Pathology, University Hospitals Plymouth NHS Trust, Plymouth, England.
Department of Neurosurgery, University Hospitals Plymouth NHS Trust, Plymouth, England; Department of Cellular & Anatomical Pathology, University Hospitals Plymouth NHS Trust, Plymouth, England.
出版信息
World Neurosurg. 2020 May;137:239-242. doi: 10.1016/j.wneu.2020.01.229. Epub 2020 Feb 5.
BACKGROUND
Rosai-Dorfman disease (RDD) is a rare idiopathic benign proliferative disorder of histiocytes, predominantly affecting the lymph nodes. RDD can also present in extranodal tissues and is occasionally found within the central nervous system.
CASE DESCRIPTION
We report the case of a 52-year-old man presenting with a short episode of dizziness. Imaging identified a right frontal, extraaxial, dural-based lesion, suspicious for a meningioma. The patient underwent a craniotomy for tumor resection and, although not entirely typical, the pathology was consistent with RDD. No other evidence of RDD was identified.
CONCLUSIONS
RDD should be considered as a differential diagnosis of dural-based lesions, more commonly meningiomas.
背景
罗萨-多夫曼病（RDD）是一种罕见的组织细胞增生性疾病，病因不明，主要影响淋巴结。RDD 也可发生在结外组织，偶尔也可发生在中枢神经系统内。
病例描述
我们报告了一例 52 岁男性，表现为短暂的头晕。影像学检查发现右侧额部、颅外、硬脑膜基底部病变，疑似脑膜瘤。患者接受了开颅肿瘤切除术，尽管不完全典型，但病理结果符合 RDD。未发现其他 RDD 的证据。
结论
RDD 应被视为硬脑膜基底部病变的鉴别诊断，更常见的是脑膜瘤。
Zotero 插件