• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

视神经脊髓炎谱系疾病伴严重体位性低血压,源于下丘脑病变。

Neuromyelitis optica spectrum disorder with severe orthostatic hypotension due to hypothalamic lesions.

机构信息

Department of Neurology, Teikyo University School of Medicine, Kaga 2-11-1, Itabashi-ku, Tokyo 1738605, Japan.

Department of Neurology, Teikyo University School of Medicine, Kaga 2-11-1, Itabashi-ku, Tokyo 1738605, Japan.

出版信息

Mult Scler Relat Disord. 2020 May;40:101977. doi: 10.1016/j.msard.2020.101977. Epub 2020 Jan 31.

DOI:10.1016/j.msard.2020.101977
PMID:32036263
Abstract

BACKGROUND

Rare cases of neuromyelitis optica spectrum disorder (NMOSD) occur with only hypothalamic lesions as the initial lesion, and such cases can present with hypersomnia, endocrinopathy, and autonomic failure. However, orthostatic hypotension (OH) caused by hypothalamic lesions due to NMOSD has not been reported.

CASE REPORT

We report the case of a patient with NMOSD who presented with severe OH due to hypothalamic lesions.

CONCLUSION

We suggest that clinicians should be aware that NMOSD with hypothalamic lesions can present with OH.

摘要

背景

极罕见情况下,视神经脊髓炎谱系疾病(NMOSD)仅以下丘脑病变为首发表现,此类病例可出现嗜睡、内分泌异常和自主神经衰竭。然而,NMOSD 所致下丘脑病变引起的直立性低血压(OH)尚未见报道。

病例报告

我们报告了一例 NMOSD 患者,因下丘脑病变出现严重 OH。

结论

我们建议临床医生应注意到,伴有下丘脑病变的 NMOSD 可出现 OH。

相似文献

1
Neuromyelitis optica spectrum disorder with severe orthostatic hypotension due to hypothalamic lesions.视神经脊髓炎谱系疾病伴严重体位性低血压,源于下丘脑病变。
Mult Scler Relat Disord. 2020 May;40:101977. doi: 10.1016/j.msard.2020.101977. Epub 2020 Jan 31.
2
Sudden onset of sleep due to hypothalamic lesions in neuromyelitis optica spectrum disorder positive for anti-aquaporin-4 antibody.抗水通道蛋白 4 抗体阳性的视神经脊髓炎谱系疾病患者因下丘脑病变而突然入睡。
Mult Scler. 2014 Sep;20(10):1407-8. doi: 10.1177/1352458514540359.
3
Hypersomnia as an isolated symptom of neuromyelitis optica.发作性睡病作为视神经脊髓炎的孤立症状。
Intern Med J. 2018 Dec;48(12):1546-1547. doi: 10.1111/imj.14118.
4
Neuromyelitis optica spectrum disorder presenting with repeated hypersomnia due to involvement of the hypothalamus and hypothalamus-amygdala linkage.视神经脊髓炎谱系障碍因下丘脑及下丘脑 - 杏仁核联系受累而出现反复性嗜睡。
Mult Scler. 2015 Jun;21(7):960-2. doi: 10.1177/1352458515569100. Epub 2015 Feb 13.
5
[A case of neuromyelitis optica spectrum disorder presenting with severe orthostatic hypotension].1例以严重直立性低血压为表现的视神经脊髓炎谱系障碍病例
Rinsho Shinkeigaku. 2015;55(10):759-62. doi: 10.5692/clinicalneurol.cn-000702. Epub 2015 Aug 18.
6
Galactorrhea in a Patient With Aquaporin-4 Antibody-positive Neuromyelitis Optica Spectrum Disorder: A Case Report and Review of the Literature.水通道蛋白4抗体阳性视神经脊髓炎谱系障碍患者的溢乳:一例报告及文献复习
Neurologist. 2015 Dec;20(6):101-3. doi: 10.1097/NRL.0000000000000061.
7
Secondary hypersomnia as an initial manifestation of neuromyelitis optica spectrum disorders.以继发性嗜睡症为首发表现的视神经脊髓炎谱系疾病。
Mult Scler Relat Disord. 2020 Feb;38:101869. doi: 10.1016/j.msard.2019.101869. Epub 2019 Nov 25.
8
[Clinical characteristics and follow-up of pediatric patients with neuromyelitis optica and neuromyelitis optica spectrum disorders].视神经脊髓炎及视神经脊髓炎谱系障碍患儿的临床特征与随访
Zhonghua Er Ke Za Zhi. 2015 Apr;53(4):268-73.
9
[Neuromyelitis optica with syndrome of inappropriate secretion of antidiuretic hormone and hypersomnia associated with bilateral hypothalamic lesions: a case report].[视神经脊髓炎伴抗利尿激素分泌不当综合征及与双侧下丘脑病变相关的嗜睡症:一例报告]
Rinsho Shinkeigaku. 2011 Aug;51(8):599-602. doi: 10.5692/clinicalneurol.51.599.
10
[A case of suspected neuromyelitis optica spectrum disorder preceded by aseptic meningitis-like symptoms].[一例以无菌性脑膜炎样症状为先兆的疑似视神经脊髓炎谱系障碍病例]
Rinsho Shinkeigaku. 2019 Nov 8;59(11):736-739. doi: 10.5692/clinicalneurol.cn-001316. Epub 2019 Oct 26.

引用本文的文献

1
Severe orthostatic hypotension associated with lesions of the area postraema in neuromyelitis optica spectrum disorder.视神经脊髓炎谱系障碍中与后索病变相关的严重直立性低血压。
eNeurologicalSci. 2021 Mar 8;23:100335. doi: 10.1016/j.ensci.2021.100335. eCollection 2021 Jun.