Department of Pediatric Cardiology, University of Health Sciences, Diyarbakır Gazi Yasargil Training and Research Hospital, Diyarbakır, Turkey.
Department of Pediatric Cardiology, Faculty of Medicine, University of Başkent, Ankara, Turkey.
Cardiol Young. 2020 Mar;30(3):409-412. doi: 10.1017/S1047951120000244. Epub 2020 Feb 17.
Double-chambered right ventricle is characterised by division of the outlet portion of the right ventricle by hypertrophy of the septoparietal trabeculations into two parts. We aim to report our experiences regarding the presenting symptoms of double-chambered right ventricle, long-term prognosis, including the recurrence rate and incidence of arrhythmias after surgery.
We retrospectively investigated 89 consecutive patients who were diagnosed to have double-chambered right ventricle and underwent a surgical intervention from 1995 to 2016. The data obtained by echocardiography, cardiac catheterisation, and surgical findings as well as post-operative follow-up, surgical approaches, post-operative morbidity, mortality, and cardiac events were evaluated.
Median age at the time of diagnosis was 2 months and mean age at the time of operation was 5.3 years. Concomitant cardiac anomalies were as follows: perimembranous ventricular septal defect (78 patients), atrial septal defect (9 patients), discrete subaortic membrane (32 patients), right aortic arch (3 patients), aortic valve prolapse and/or mild aortic regurgitation (14 patients), and left superior caval vein (2 patients). The mean follow-up period was 4.86 ± 4.6 years. In these patients, mean systolic pressure gradient in the right ventricle by echocardiography before, immediately, and long-term after surgical intervention was 66.3, 11.8, and 10.4 mmHg, respectively. There were no deaths during the long-term follow-up period. Surgical reinterventions were performed for residual ventricular septal defect (2), residual pulmonary stenosis (1), and severe tricuspid insufficiency (1).
The surgical outcomes and prognosis of double-chambered right ventricle are favourable, recurrence and fatal arrhythmias are unlikely in long-term follow-up.
双心室右心室的特征是由于室间隔隔束肥厚，将右心室的出口部分分为两部分。我们旨在报告我们在双心室右心室的临床表现、长期预后，包括手术后心律失常的复发率和发生率方面的经验。
我们回顾性研究了 1995 年至 2016 年间诊断为双心室右心室并接受手术干预的 89 例连续患者。评估了通过超声心动图、心导管检查和手术发现以及术后随访、手术方法、术后发病率、死亡率和心脏事件获得的数据。
诊断时的中位年龄为 2 个月，手术时的平均年龄为 5.3 岁。并存的心脏畸形如下：膜周室间隔缺损（78 例）、房间隔缺损（9 例）、离散的主动脉下膜（32 例）、右主动脉弓（3 例）、主动脉瓣脱垂和/或轻度主动脉瓣反流（14 例）和左上腔静脉（2 例）。平均随访时间为 4.86±4.6 年。在这些患者中，超声心动图检查右心室收缩期压力梯度术前、即刻和术后长期分别为 66.3、11.8 和 10.4mmHg。在长期随访期间无死亡。再次手术干预的原因是残余室间隔缺损（2 例）、残余肺动脉瓣狭窄（1 例）和严重三尖瓣关闭不全（1 例）。
双心室右心室的手术结果和预后良好，长期随访中不太可能出现心律失常复发和致命性心律失常。
