Zhang Heping, Liu Fangyun, Wei Jianguo, Xue Debin, Xie Zhengxin, Xu Chunwei
Department of Pathology, Anhui Province Maternal and Child Health Hospital, Hefei 230001, People's Republic of China.
FenLan Medical Lab, Hangzhou 310052, People's Republic of China.
Open Med (Wars). 2020 Feb 4;15:65-70. doi: 10.1515/med-2020-0010. eCollection 2020.
Germ cell tumors (GCTs) localized extragonadally are rare, with only 14 reported cases of a yolk sac tumor in the endometrium. Here we report a case of mixed endometrium GCTs in a 65-year-old postmenopausal woman with abnormal vaginal bleeding. An ultrasound examination showed an oval-shaped mass in the patient's uterine cavity. Biochemical examination revealed elevated serum α-fetoprotein (AFP) at 359 ng/mL, whereas the tumor markers CA-125, CA-199, and CEA were all within normal range. Total hysterectomy and bilateral salpingo-oophorectomy were performed;. a histological examination revealed that the malignant components contained a yolk sac tumor, embryonal carcinoma, and focal immature teratoma. Immunohistochemical staining showed that AFPs were diffusively distributed in both the yolk sac tumor and embryonal carcinoma. The stem cell marker OCT3/4 was positive in the embryonal carcinoma component and that the pan-cytokeratin AE1/AE3 staining was positive in glandular areas. GFAPs (Glial Fibrillary Acidic Proteins) were positive in neuroectodermal tubules; the Ki-67 protein was positive in 90% of the tumor cells, whereas CD117 and placental alkaline phosphatase (PLAP) were negative. The cumulative evidence indicated mixed GCTs of endometrium as the final histopathological diagnosis. The patient received three courses of adjunct chemotherapy that provided good therapeutic efficacy as evidenced by the decreased serum AFP level. Our report on this rare case of mixed GCTs of the endometrium, supported by associated histological patterns and immunophenotypes and successful adjunct chemotherapy after surgery, could provide insight on future treatment of this rare but lethal disease.
性腺外局限性生殖细胞肿瘤(GCTs)较为罕见,子宫内膜卵黄囊瘤仅有14例报道。本文报告一例65岁绝经后阴道出血异常的女性发生的混合性子宫内膜GCTs病例。超声检查显示患者宫腔内有一椭圆形肿块。生化检查显示血清甲胎蛋白(AFP)升高至359 ng/mL,而肿瘤标志物CA-125、CA-199和癌胚抗原(CEA)均在正常范围内。行全子宫切除术和双侧输卵管卵巢切除术;组织学检查显示恶性成分包含卵黄囊瘤、胚胎性癌和局灶性未成熟畸胎瘤。免疫组化染色显示AFP在卵黄囊瘤和胚胎性癌中均呈弥漫性分布。干细胞标志物OCT3/4在胚胎性癌成分中呈阳性,全细胞角蛋白AE1/AE3染色在腺区呈阳性。胶质纤维酸性蛋白(GFAPs)在神经外胚层小管中呈阳性;Ki-67蛋白在90%的肿瘤细胞中呈阳性,而CD117和胎盘碱性磷酸酶(PLAP)呈阴性。累积证据表明最终组织病理学诊断为子宫内膜混合性GCTs。患者接受了三个疗程的辅助化疗,血清AFP水平下降证明化疗疗效良好。我们对这例罕见的子宫内膜混合性GCTs病例的报告,辅以相关组织学模式和免疫表型以及术后成功的辅助化疗,可为这种罕见但致命疾病的未来治疗提供见解。