Vadhul Raghav, Halbach Caroline S, Areaux Raymond G, Berry Susan, Hou Joshua H
Indiana University School of Medicine, Indianapolis.
Department of Ophthalmology and Visual Neurosciences, University of Minnesota, Minneapolis.
Digit J Ophthalmol. 2019 Nov 17;25(4):59-64. doi: 10.5693/djo.02.2019.09.001. eCollection 2019 Apr.
A 4-year-old girl with a history of Pearson marrow-pancreas syndrome presenting with severe, progressive photophobia was found to have bilateral, diffuse corneal thickening and peripheral pigmentary retinopathy. She underwent Descemet stripping automated endothelial keratoplasty (DSAEK) surgery in both eyes using a modified suture pull-through technique. Postoperatively there was no evidence of cataract formation or graft detachment; her corneas thinned, and her photophobia improved dramatically.
一名患有皮尔逊骨髓-胰腺综合征的4岁女孩,出现严重的进行性畏光症状,被发现双眼弥漫性角膜增厚及周边色素性视网膜病变。她双眼接受了使用改良缝线牵拉技术的后弹力层剥除自动角膜内皮移植术(DSAEK)。术后未发现白内障形成或移植物脱离的迹象;她的角膜变薄,畏光症状显著改善。