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皮肌炎与结节病相关的肉芽肿性肌病。

Dermatomyositis and granulomatous myopathy associated with sarcoidosis.

作者信息

Lipton J H, McLeod B D, Brownell A K

机构信息

Department of Medicine, Faculty of Medicine, University of Calgary, Alberta, Canada.

出版信息

Can J Neurol Sci. 1988 Nov;15(4):426-9.

PMID:3208229
Abstract

A previously healthy, 21-year-old female presented with acute dermatomyositis. Chest X-ray revealed bilateral hilar adenopathy, and mediastinal lymph node biopsy demonstrated noncaseating granulomata compatible with sarcoidosis. The patient improved spontaneously. The significance of bilateral hilar adenopathy in association with dermatomyositis and implications for management are discussed.

摘要

一名既往健康的21岁女性出现急性皮肌炎。胸部X线显示双侧肺门淋巴结肿大,纵隔淋巴结活检显示非干酪样肉芽肿,符合结节病表现。患者症状自行改善。本文讨论了双侧肺门淋巴结肿大与皮肌炎相关的意义及对治疗的启示。

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