D'Elia Marcella Leal Novello, Park Kelly K, Weiss Eduardo
Dr. D'Elia is with the Department of Dermatology at Pedro Ernesto University Hospital (HUPE) of Rio de Janeiro State University (UERJ) in Rio de Janeiro, Brazil.
Dr. Park is with Edward Hines, Jr. Veterans Affairs Medical Center in Hines, Illinois and is an Affiliate Faculty Member at Loyola University Stritch School of Medicine.
J Clin Aesthet Dermatol. 2020 Jan;13(1):35-37. Epub 2020 Jan 1.
Acral myxoinflammatory fibroblastic sarcoma (AMFS) represents a low-grade sarcoma with a high rate of local recurrence that commonly affects the distal extremities. The lesion often presents as a painless mass in the hands or feet. There is no formal standardized treatment protocol for this tumor, but wide surgical excision, with or without adjuvant radiation therapy, is the conventional treatment. We report a case of a patient with an AMFS treated with Mohs micrographic surgery (MMS) without recurrence. Because of the propensity of this tumor to involve acral sites where tissue conservation is important, MMS might be an alternative treatment modality for this rare entity.
肢端黏液炎性纤维母细胞肉瘤（AMFS）是一种低度恶性肉瘤，局部复发率高，常累及四肢远端。该病变通常表现为手足部无痛性肿块。目前尚无针对此肿瘤的正式标准化治疗方案，但广泛手术切除，无论是否联合辅助放疗，是传统的治疗方法。我们报告1例采用莫氏显微外科手术（MMS）治疗且未复发的AMFS患者。鉴于此肿瘤倾向于累及对组织保留很重要的肢端部位，MMS可能是这种罕见疾病的一种替代治疗方式。
