Lang Jason E, Dodd Leslie, Martinez Salutario, Brigman Brian E
Department of Radiology, Duke University Medical Center, Durham, North Carolina 27710, USA.
Clin Orthop Relat Res. 2006 Apr;445:254-60. doi: 10.1097/01.blo.0000201158.67443.a2.
During the past 2 years, we treated five patients with acral myxoinflammatory fibroblastic sarcoma at our institution. Four patients presented with a firm, painless mass in the hand that appeared over several months. One patient discovered a painless mass in his shoulder region. The five patients initially were diagnosed as having benign conditions and treated with intralesional or marginal excision by referring physicians, only to have the lesion reappear as sarcoma. Each patient was treated with wide resection of the tumor bed. Acral myxoinflammatory fibroblastic sarcoma is a rare, but increasingly recognized sarcoma of the distal extremities, which often is confused with benign lesions. Surgeons should be familiar with this tumor's clinical, radiographic, and histologic appearances as it has a high rate of recurrence and can metastasize.
在过去两年中，我们机构治疗了5例肢端黏液炎性纤维母细胞肉瘤患者。4例患者手部出现质地硬、无痛性肿块，持续数月。1例患者在肩部区域发现无痛性肿块。这5例患者最初被转诊医生诊断为良性疾病，并接受了病损内或边缘切除治疗，但病变后来均复发为肉瘤。每位患者均接受了肿瘤床的广泛切除。肢端黏液炎性纤维母细胞肉瘤是一种罕见但越来越被认识到的远端肢体肉瘤，常与良性病变相混淆。由于其复发率高且可发生转移，外科医生应熟悉该肿瘤的临床、影像学和组织学表现。
