Whitlow Shane, Idrees Zubair
Department of Ophthalmology, Cork University Hospital, Cork, Ireland.
Am J Ophthalmol Case Rep. 2019 Sep 13;17:100554. doi: 10.1016/j.ajoc.2019.100554. eCollection 2020 Mar.
To report a case of a woman who had Ehlers Danlos syndrome who developed a bullous retinal detachment.
A 33-year-old Caucasian woman presented with 1-day history of floaters and photopsia. Patient had extensive scleral ectasia. Scleral buckle could not be performed due the severity of the ectasia. Patient had a vitrectomy and subsequently had multiple re-detachments with sclera ruptures during the retinal detachment repairs. Patient required a 360-degree scleral patch graft to prevent scleral ruptures during the vitrectomy. Patient has a stable flat report 7 months post-op with vision of 1/60.
This is the first case report of a patient requiring a 360-degree scleral patch graft. This option should be considered to assist in preventing scleral ruptures, intraoperatively and post operatively in patient who have an increased risk of scleral rupture, such as patients with connective tissue disorders.
报告1例患有埃勒斯-当洛综合征（Ehlers Danlos syndrome）并发生大泡性视网膜脱离的女性病例。
一名33岁的白种女性，有1天的飞蚊症和闪光感病史。患者存在广泛的巩膜扩张。由于巩膜扩张严重，无法进行巩膜扣带术。患者接受了玻璃体切除术，随后在视网膜脱离修复过程中多次发生再脱离并伴有巩膜破裂。患者需要进行360度巩膜补片移植，以防止玻璃体切除术中巩膜破裂。术后7个月患者视网膜复位稳定，视力为1/60。
这是首例需要进行360度巩膜补片移植的病例报告。对于巩膜破裂风险增加的患者，如患有结缔组织疾病的患者，应考虑采用此方法来协助预防术中及术后的巩膜破裂。
