Kazaz Ilke Onur, Ersoz Safak, Colak Fatih, Teoman Ahmet Serdar, Kazaz Seher Nazli, Karaguzel Ersagun, Kutlu Omer
Department of Urology and Pathology, Karadeniz Technical University Faculty of Medicine, Trabzon, Turkey.
Department of Urology, Trabzon Fatih State Hospital, Trabzon, Turkey.
Indian J Pathol Microbiol. 2020 Feb;63(Supplement):S44-S46. doi: 10.4103/IJPM.IJPM_66_19.
Primary renal angiosarcomas (AS) are uncommon tumors with poor prognosis. Aetiology is unknown but some unproven risk factors have been described. It is difficult to discriminate these masses from renal cell carcinomas or other renal masses with imaging modalities. Immunohistochemistry plays an important role in the diagnosis. Main treatment protocol for primary renal AS is still controversial and nephrectomy with chemotherapy and/or radiotherapy seems the only treatment option. We state a primary renal angiosarcoma case for its rareness and contribution to literature.
原发性肾血管肉瘤（AS）是一种罕见的肿瘤，预后较差。病因不明，但已描述了一些未经证实的危险因素。通过影像学检查很难将这些肿块与肾细胞癌或其他肾脏肿块区分开来。免疫组织化学在诊断中起着重要作用。原发性肾AS的主要治疗方案仍存在争议，肾切除术加化疗和/或放疗似乎是唯一的治疗选择。我们报告一例原发性肾血管肉瘤病例，因其罕见性及对文献的贡献。
