Foresti V, Villa A, Parisio E, Castini D
Ospedale Fatebenefratelli e Oftalmico, Milano, Divisione Medica III.
Minerva Med. 1988 Dec;79(12):1109-12.
A case of a patient with clinical picture of hepatosplenomegaly, portal hypertension, dilatation of hepatic veins and inferior vena cava, without venous thrombosis or other causes of obstruction of right-sided heart, is described. This picture is compatible with the Budd-Chiari syndrome. Echocardiography has shown a hypertrophic cardiomyopathy causing relevant dilatation of both atria and it has allowed us to exclude the presence of a constrictive pericarditis. The hypertrophic cardiomyopathy is first considered as a cardiac cause of cirrhosis mimicking the Budd-Chiari syndrome.
本文描述了一例患者,其临床表现为肝脾肿大、门静脉高压、肝静脉和下腔静脉扩张,无静脉血栓形成或其他导致右心梗阻的原因。此表现符合布加综合征。超声心动图显示肥厚型心肌病导致双房明显扩张,并排除了缩窄性心包炎的存在。肥厚型心肌病首先被认为是模拟布加综合征的肝硬化的心脏病因。