Hori A, Fiebig I, Stichnoth F A
Département de Neuropathologie, Université de Goettingen.
Ann Pathol. 1988;8(4-5):321-4.
The accompanying central nervous system (CNS) malformation in thoracoabdominal evisceration syndrome has up till now not been given much attention. Two such cases in the early fetal stages are demonstrated here, in which CNS anomalies were severely dysraphic. It is possible that babies with the evisceration syndrome are less capable of surviving when the CNS complication is severe. This may well be the reason why CNS complication of the syndrome has seldom been observed.
迄今为止,胸腹脏器外翻综合征所伴发的中枢神经系统(CNS)畸形尚未得到足够重视。本文展示了两例早期胎儿阶段的此类病例,其中中枢神经系统异常为严重的神经管闭合不全。当CNS并发症严重时,脏器外翻综合征患儿的存活能力可能较低。这很可能就是该综合征的CNS并发症很少被观察到的原因。