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两例慢性脑脊髓炎尸检病例:神经白塞病的变异型?

Two necropsy cases of chronic encephalomyelitis: variants of Neuro-Behçet's syndrome?

作者信息

Iseki E, Iwabuchi K, Yagishita S, Amano N, Matsushita M

机构信息

Department of Psychiatry and Neurology, Yokohama City University School of Medicine, Japan.

出版信息

J Neurol Neurosurg Psychiatry. 1988 Aug;51(8):1084-7. doi: 10.1136/jnnp.51.8.1084.

Abstract

Two necropsy cases of chronic encephalomyelitis of unknown aetiology are presented. Skin hyperreactivity occurred in both cases although there were no mucocutaneo-ocular symptoms. There was confluent perivenous necrosis with marked glio-mesenchymal reactions and persistent inflammatory changes, predominantly in the diencephalon and brain stem. These cases are clinico-pathologically analogous to Neuro-Behcet's syndrome.

摘要

本文报告了两例病因不明的慢性脑脊髓炎尸检病例。尽管没有黏膜皮肤眼部症状,但两例均出现皮肤高反应性。有融合性静脉周围坏死,伴有明显的胶质-间充质反应和持续性炎症改变,主要累及间脑和脑干。这些病例在临床病理上与神经白塞病相似。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1d0b/1033120/028d84180543/jnnpsyc00543-0069-a.jpg

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