Migkos Michail P, Sarmas Ioannis, Somarakis George A, Voulgari Paraskevi V, Tsamis Konstantinos I, Drosos Alexandros A
Rheumatology Clinic, Department of Internal Medicine, Medical School, University of Ioannina, Ioannina Greece.
Neurosurgical Institute, University of Ioannina School of Medicine, Ioannina, Greece; Department of Neurology, University Hospital of Ioannina, Ioannina, Greece.
Mediterr J Rheumatol. 2018 Jun 29;29(2):92-96. doi: 10.31138/mjr.29.2.92. eCollection 2018 Jun.
Sjögren's syndrome (SS) is a chronic autoimmune inflammatory disorder characterized by diminished lacrimal and salivary gland function that may affect multiple organ systems. The association of SS with inflammatory myopathies (IM), a group of diseases characterized by chronic inflammation of striated muscle and skin has been infrequently described.
We present two cases diagnosed with SS who developed IM. We have also conducted a review of the English literature to depict all available clinical evidence on the clinical association of SS with IM.
Two female patients diagnosed with SS developed polymyositis (PM) and inclusion body myositis (IBM) respectively. The literature review identified 24 cases with coexistence of the two autoimmune conditions (SS and IM). Twenty-two patients were females and two males. Eight patients were diagnosed with IBM, 15 were diagnosed with PM and 1 with dermatomyositis. All patients had biopsy proven IM.
There is evidence of clinical association of primary SS and IM especially with IBM and PM. Patients with SS and symptoms of muscle weakness should be investigated for associated IM.
干燥综合征(SS)是一种慢性自身免疫性炎症性疾病,其特征为泪腺和唾液腺功能减退,可能影响多个器官系统。SS与炎性肌病(IM)(一组以横纹肌和皮肤慢性炎症为特征的疾病)之间的关联鲜有报道。
我们报告了2例诊断为SS并发展为IM的病例。我们还对英文文献进行了综述,以描述关于SS与IM临床关联的所有现有临床证据。
2例诊断为SS的女性患者分别发展为多发性肌炎(PM)和包涵体肌炎(IBM)。文献综述确定了24例同时存在这两种自身免疫性疾病(SS和IM)的病例。22例为女性,2例为男性。8例诊断为IBM,15例诊断为PM,1例诊断为皮肌炎。所有患者均经活检证实为IM。
有证据表明原发性SS与IM存在临床关联,尤其是与IBM和PM。有SS且伴有肌无力症状的患者应进行相关IM的检查。