Dominguez F E, Tate L G, Robinson M J
Mount Sinai Medical Center, Miami Beach, Florida.
Am J Cardiovasc Pathol. 1988;2(3):269-72.
Fibromuscular dysplasia involving the aorta, its main arch branches, and the coronary arteries is infrequent. Familial occurrence of arterial fibromuscular dysplasia is rarely recognized in infancy. We report three infant siblings with this disorder who presented with sudden unexpected death secondary to acute myocardial infarction as a complication of fibromuscular dysplasia involving the aorta, its main arch branches, and the major coronary arteries. This condition must be considered in the differential diagnosis of identifiable causes of the sudden infant death syndrome.
累及主动脉、其主要弓部分支及冠状动脉的纤维肌性发育异常并不常见。动脉纤维肌性发育异常的家族性发病在婴儿期很少被认识到。我们报告了三名患有这种疾病的婴儿兄弟姐妹，他们因累及主动脉、其主要弓部分支及主要冠状动脉的纤维肌性发育异常并发症——急性心肌梗死继发意外猝死。在鉴别诊断婴儿猝死综合征的可识别病因时必须考虑这种情况。
