Sanchez-Nadales Alejandro, Anampa-Guzman Andrea, Navarro-Motta Jessica
Department of Medicine, Advocate Illinois Masonic Medical Center, Chicago, IL, USA.
Sociedad Cientifica de San Fernando, Faculty of Medicine, Universidad Nacional Mayor de San Marcos, Lima, Peru.
Cardiol Res. 2020 Apr;11(2):118-128. doi: 10.14740/cr1025. Epub 2020 Mar 10.
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis characterized by systemic xanthogranulomatous infiltration. We described the case of a female adult presenting with pericardial effusion. Pericardial infiltration is the most frequent cardiac manifestation of ECD and is the one discussed in this article. We found that the majority of patients with pericardial infiltration needed a cardiovascular procedure.
Erdheim-Chester病(ECD)是一种罕见的非朗格汉斯细胞组织细胞增多症,其特征为全身性黄色瘤样肉芽肿浸润。我们描述了一例出现心包积液的成年女性病例。心包浸润是ECD最常见的心脏表现,也是本文所讨论的内容。我们发现,大多数有心包浸润的患者需要进行心血管手术。