Soares Raquel Reis, Ferber Leonardo, Ferber Matheus, Mata Daniel Soares
Biocor Instituto Department of Anesthesiology Nova Lima MG Brazil Department of Anesthesiology, Biocor Instituto, Nova Lima, MG, Brazil.
Universidade Federal de Minas Gerais Hospital das Clínicas Department of Cardiovascular Surgery Belo Horizonte MG Brazil Department of Cardiovascular Surgery, Hospital das Clínicas da Universidade Federal de Minas Gerais, Belo Horizonte, MG, Brazil.
Braz J Cardiovasc Surg. 2020 Feb 1;35(1):117-119. doi: 10.21470/1678-9741-2018-0403.
Congenital mitral valve stenosis is a rare and severe disease, usually associated with other heart defects. The appropriate intervention depends on the site and mechanism of valvular obstruction and the aim is to avoid or delay valve replacement since it is associated with significant morbidity and mortality. Early single-stage complete repair is associated with better prognosis. We report the case of a 20-month-old child with a supravalvar mitral ring combined with a ventricular septal defect; pulmonary arterial systolic pressure before the surgery was 79 mmHg. The patient underwent a successful surgical repair with good clinical resolution.
先天性二尖瓣狭窄是一种罕见且严重的疾病，通常与其他心脏缺陷相关。恰当的干预措施取决于瓣膜梗阻的部位和机制，目的是避免或推迟瓣膜置换，因为瓣膜置换与显著的发病率和死亡率相关。早期单阶段完全修复预后较好。我们报告一例20个月大的儿童，患有瓣上二尖瓣环合并室间隔缺损；手术前肺动脉收缩压为79 mmHg。该患者接受了成功的手术修复，临床症状得到良好缓解。
