Deli Gabriella, Hedvig Komáromy, Pál Endre, Pfund Zoltán
Pécsi Tudományegyetem, Klinikai Központ, Neurológiai Klinika, Pécs.
Pécsi Diagnosztikai Központ, Pécs.
Ideggyogy Sz. 2020 Mar 30;73(3-4):85-98. doi: 10.18071/isz.73.0085.
Diseases with peripheral motor symptoms are a rare, but important subgroup of the all peripheral neuropathies, radiculopathies and neuronopathies. In these mostly progressive neuropathies, the clinical features include pure motor symptoms with weakness and wasting of the striated muscles. The differentiation of these diseases is frequently a challenge for qualified clinical neurologists. A careful history taking, the disease time course, the findings of routine clinical physical examination and the electrophysiological studies are all necessary in the diagnostic procedure. The aim of this publication is to overview the clinical characteristics of the pure motor peripheral neuropathies, to consider the diagnostic steps and the differential diagnosis, and finally to summarize the treatment options.
伴有周围运动症状的疾病是所有周围神经病、神经根病和神经元病中一个罕见但重要的亚组。在这些大多为进行性的神经病中，临床特征包括单纯的运动症状，伴有横纹肌无力和萎缩。对合格的临床神经科医生来说，区分这些疾病常常是一项挑战。在诊断过程中，仔细询问病史、了解疾病病程、常规临床体格检查结果以及电生理研究都是必要的。本出版物的目的是概述单纯运动性周围神经病的临床特征，思考诊断步骤和鉴别诊断，最后总结治疗选择。
