表现为眼动脉阻塞的原发性血小板增多症。

Essential thrombocythemia manifesting as ophthalmic artery occlusion.

作者信息

Thabsuwan Kittipong, Chantarasorn Yodpong

机构信息

Department of Ophthalmology, Vajira Hospital, Navamindradhiraj University, 681 Samsen Street, Dusit Bangkok, 10300, Thailand.

出版信息

Am J Ophthalmol Case Rep. 2020 Apr 23;18:100724. doi: 10.1016/j.ajoc.2020.100724. eCollection 2020 Jun.

DOI:10.1016/j.ajoc.2020.100724

PMID:32373760

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7195516/

Abstract

PURPOSE

To report the first case of a patient with essential thrombocythemia (ET) who presented with unilaterally extensive choroidal ischemia coinciding with central retinal artery occlusion (CRAO).Observations: A 64-year-old man presented with a classic sign of short posterior ciliary artery (SPCA) occlusion, Amalric triangular choroidal infarction, coinciding with CRAO in the left eye. He was later diagnosed as having ET due to a massive platelet count of 1,100,000 cells/mm and confirmed genetic testing. The magnetic resonance angiogram subsequently revealed severe occlusions of neuro-ophthalmic circulation. Interestingly, occult choriocapillaris occlusions were detected in the right eye despite being visually asymptomatic.

CONCLUSION AND IMPORTANCE

Patients with ET can present with concurrent CRAO and SPCA occlusion. Identifying the causes of such events is crucial as these can precede systemic thrombocytosis or hemorrhagic complications.

摘要

目的

报告首例原发性血小板增多症（ET）患者，其出现单侧广泛脉络膜缺血并伴有视网膜中央动脉阻塞（CRAO）。观察结果：一名64岁男性出现典型的睫状后短动脉（SPCA）阻塞体征，即阿马尔里克三角形脉络膜梗死，同时左眼发生CRAO。由于血小板计数高达1,100,000个细胞/mm且基因检测确诊，他后来被诊断为ET。磁共振血管造影随后显示神经眼科循环严重阻塞。有趣的是，尽管右眼在视觉上无症状，但检测到隐匿性脉络膜毛细血管阻塞。