Clin Neuropathol. 2020 Nov/Dec;39(6):275-281. doi: 10.5414/NP301280.
Only a few cases of syndrome of inappropriate antidiuretic hormone secretion (SIADH) in the setting of amyotrophic lateral sclerosis (ALS) have been described in the literature. We present the case of an 81-year-old male who developed severe hyponatremia following elective total hip replacement. His past medical history included prostate cancer, which was under surveillance, and ischemic heart disease. He reported recent weight loss, worsening shortness of breath, and lethargy. SIADH was diagnosed on the basis of hyponatremia, elevated urinary sodium, and decreased serum osmolality, presumed secondary to surgery. Investigations revealed no occult malignancy and no other cause for hyponatremia. He was discharged when sodium levels had normalized, however, he then had several further admissions for hyponatremia, general fatigue, and breathlessness. His condition continued to decline, and he developed dysphagia, weakness, and tongue fasciculations. Neurological examination showed globally decreased power, increased tone, and fasciculations. MRI of the brain was normal. He did not respond to neostigmine treatment, and a presumed diagnosis of motor neuron disease was made. The patient passed away shortly after this, and a post-mortem confirmed the diagnosis of ALS. Drug, post-operative, and cancer-related causes were precluded by the timing of onset of hyponatremia. We present this case and an analysis of previously published cases alongside a discussion on the potential causative mechanisms.
仅有少数几例肌萎缩侧索硬化症(ALS)合并抗利尿激素分泌不当综合征(SIADH)的病例在文献中被描述。我们报告了一例 81 岁男性的病例,他在接受择期全髋关节置换术后出现严重低钠血症。他的既往病史包括正在接受监测的前列腺癌和缺血性心脏病。他报告了最近的体重减轻、呼吸困难加重和乏力。根据低钠血症、尿钠升高和血清渗透压降低,诊断为 SIADH,推测与手术有关。检查未发现隐匿性恶性肿瘤和其他导致低钠血症的原因。当钠离子水平正常化后,他出院了,但随后又因低钠血症、全身疲劳和呼吸困难多次入院。他的病情持续恶化,出现吞咽困难、无力和舌肌抽搐。神经检查显示全身肌力下降、肌张力增高和肌束震颤。脑部 MRI 正常。他对新斯的明治疗无反应,被诊断为运动神经元病。此后不久,患者去世,尸检证实了 ALS 的诊断。药物、术后和癌症相关的原因可以根据低钠血症的发病时间来排除。我们提出了这个病例,并对之前发表的病例进行了分析,并讨论了潜在的致病机制。