Franconeri Andrea, Ballati Francesco, Pin Maurizio, Carone Luisa, Danesino Gian M, Valentini Adele
Department of Radiology, IRCCS Policlinico San Matteo Foundation, Pavia, Italy.
Department of Clinical-Surgical, Diagnostic and Pediatric Sciences, University of Pavia, Pavia, Italy.
Indian J Radiol Imaging. 2020 Jan-Mar;30(1):81-83. doi: 10.4103/ijri.IJRI_273_19. Epub 2020 Mar 30.
Interrupted aortic arch diagnosed in adult age is a rare entity, with only a few cases published in the literature. Most of them are classified as type A interrupted aortic arch and differential diagnosis is associated with severe chronic coarctation. We present a case of a 52-year-old woman accessed to the emergency department for chest and right upper limb pain that increased in the last days. She underwent a computed tomography angiogram showing interruption of the aortic arch, distal to left subclavian artery origin, large bilateral collateral vessels connecting subclavian arteries to descending aorta with multiple voluminous aneurysms, a bicuspid aortic valve, dilatated tubular segment of ascending thoracic aorta, and a suspected atrial septal defect. A nonsystematic literature review regarding these conditions has been performed.
成年期诊断出的主动脉弓中断是一种罕见病症,文献中仅发表了少数病例。其中大多数被归类为A型主动脉弓中断,鉴别诊断与严重的慢性缩窄有关。我们报告一例52岁女性因胸痛和右上肢疼痛前来急诊科就诊,症状在过去几天有所加重。她接受了计算机断层血管造影,结果显示主动脉弓中断,位于左锁骨下动脉起源的远端,有粗大的双侧侧支血管将锁骨下动脉与降主动脉相连,伴有多个巨大动脉瘤,还有一个二叶式主动脉瓣、升胸主动脉的扩张管状段以及一个疑似房间隔缺损。我们对这些病症进行了非系统性的文献综述。