Kim Yong Yean, Wynn Tung Thanh, Reith John David, Slayton William B, Lagmay Joanne, Fort John, Rajderkar Dhanashree Abhijit
National Cancer Institute, Pediatric Oncology Branch, 37 Convent Dr, Bethesda, MD 20892, USA.
University of Florida, Department of Pediatric Hematology/Oncology, Gainesville, FL 32610, USA.
Radiol Case Rep. 2020 May 24;15(7):1110-1114. doi: 10.1016/j.radcr.2020.05.016. eCollection 2020 Jul.
Primary pulmonary artery sarcoma (PAS) is extremely rare in children. Nevertheless, distinguishing primary PAS from pulmonary embolism is critical to a child's survival. Primary PAS is commonly misdiagnosed as a pulmonary embolism due to similar presenting symptoms and radiographic findings. However, compared to adults, pulmonary embolism is rare in children, especially in patients who do not have predisposing factors or hypercoagulable state. We present a child with primary PAS which mimicked pulmonary embolism on presentation but eventually was resected and is doing well 5 years after resection. In the absence of predisposing factors or hypercoagulable state, solid tumors such as primary PAS should be considered when assessing a pediatric patient with presumed pulmonary embolism.
原发性肺动脉肉瘤（PAS）在儿童中极为罕见。然而，区分原发性PAS与肺栓塞对儿童的生存至关重要。由于临床表现和影像学表现相似，原发性PAS常被误诊为肺栓塞。然而，与成人相比，肺栓塞在儿童中很少见，尤其是在没有易感因素或高凝状态的患者中。我们报告一名患有原发性PAS的儿童，其在就诊时表现类似肺栓塞，但最终接受了手术切除，术后5年情况良好。在没有易感因素或高凝状态的情况下，评估疑似肺栓塞的儿科患者时应考虑原发性PAS等实体瘤。
