Lanser Haley C., Puckett Yana
Orlando Health Cancer Institute, Orlando, Florida
Multiple biliary duct hamartomas or “von Meyenburg complexes” are rare, benign liver malformations characterized by cystic dilated biliary ducts that were first discovered in 1918 by Von Meyenburg. They are usually incidentally found at autopsy or laparotomy due to the asymptomatic clinical course. They are usually diagnosed on imaging as single or multiple small cystic nodules ranging from 0.05 cm to 1.5 cm in size. Although incidental findings can mimic metastatic liver disease as well as other clinically significant diseases, which may prompt an extensive diagnostic work-up and even surgical intervention. Thus, proper diagnosis with specific imaging findings or confirmation with histological evaluation is required.
多发性胆管错构瘤或“冯·迈恩伯格复合体”是罕见的良性肝脏畸形,其特征为胆管呈囊性扩张,于1918年由冯·迈恩伯格首次发现。由于临床过程无症状,它们通常在尸检或剖腹手术时偶然发现。它们通常在影像学上被诊断为单个或多个小囊性结节,大小从0.05厘米到1.5厘米不等。尽管偶然发现可能会模仿肝转移瘤以及其他具有临床意义的疾病,这可能会促使进行广泛的诊断检查甚至手术干预。因此,需要通过特定的影像学表现进行正确诊断或通过组织学评估进行确认。